Hypertrophic cardiomyopathy/Obstructive cardiomyopathy Anita Deane - - PowerPoint PPT Presentation

hypertrophic cardiomyopathy obstructive cardiomyopathy
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Hypertrophic cardiomyopathy/Obstructive cardiomyopathy Anita Deane - - PowerPoint PPT Presentation

Hypertrophic cardiomyopathy/Obstructive cardiomyopathy Anita Deane Snr Cardiac Physiologist Apical HCM Apical HCM Apical HCM Lateral/Inferior wall HCM Lat/Inf wall HCM HOCM Hypertrophic obstructive cardiomyopathy HOCM HOCM HOCM


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Hypertrophic cardiomyopathy/Obstructive cardiomyopathy

Anita Deane Snr Cardiac Physiologist

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Apical HCM

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Apical HCM

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Apical HCM

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Lateral/Inferior wall HCM

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Lat/Inf wall HCM

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HOCM – Hypertrophic obstructive cardiomyopathy

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HOCM

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HOCM

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HOCM

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HOCM

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HOCM

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HOCM

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HOCM

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HCM prevalence

  • Common inherited cardiovascular disease.
  • HCM, 1:500 prevalence in general population.
  • HCM most common cause of SCD in young

people, (<35 years) and athletes.

  • Autosomal dominant, child has 50% chance of

inheritance.

  • Alterations of MYH7 and MYBPC3 a/c for

>80%.

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LVOT obstruction

Valsalva manoeuvre can alter loading conditions and contractile state of the heart. However, this underestimates gradients compared with exercise, 40% sensitive in predicting exercise induced gradients. Exercise is the most physiological and sensitive method for detecting provocable LVOT

  • bstruction.
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Mimics

  • LVOT obstructive

gradient is seen in late systole.

  • Mitral regurgitation is

seen from from early systole.

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Other echo features

  • Elongated MV leaflets sometimes seen
  • Diastolic dysfunction.
  • Dilated left atrium.
  • Over time LV systolic impairment.
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Screening/Follow up? Treatment?

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Thank you, any questions?