10/31/2013 No disclosures Cochlear Implants: Where weve been, - - PDF document

10 31 2013
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10/31/2013 No disclosures Cochlear Implants: Where weve been, - - PDF document

10/31/2013 No disclosures Cochlear Implants: Where weve been, Where we are Colleen Polite, AuD Assistant Director Cochlear Implant Center Otolaryngology Head and Neck Surgery University of California, San Francisco November 1, 2013


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Cochlear Implants: Where we’ve been, Where we are

Colleen Polite, AuD Assistant Director Cochlear Implant Center Otolaryngology Head and Neck Surgery University of California, San Francisco

November 1, 2013

  • No disclosures

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Objectives

  • Candidacy Criteria
  • Cases Warranting Referral
  • Emerging Indications

Poll: I work with CIs in my practice

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Poll: How many CI candidates have you seen in ... Poll: How many patients have you referred for ...

AudiologyNOW 2008 Survey

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10 20 30 40 50 60 Saw None Saw 1‐4 Ref'd None Ref'd 1‐4

Population Statistics

  • 1,000,000 potential CI candidates in US
  • 7.5% of people who could benefit from CI have
  • ne
  • 3% of audiograms met FDA criteria for CI

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Huart, 2009

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Consumer Survey

  • Average time from onset of severe-profound

hearing loss to CI = 12 years

  • Average time from learning about CI and

discovering eligibility to surgery <1 year

  • Almost 80% of CI recipients said they would

have gotten a CI earlier if they had known about it

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Market

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ENT-VSL-3.2 Increase the proportion of persons who are deaf or very hard of hearing and who have cochlear implants

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Baseline: 76.8 per 10,000 persons Target: 84.7 per 10,000 persons

10 percent improvement

www.healthypeople.gov/2020

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Where we’ve been

Bilger Report, 1977

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  • Benefits lipreading
  • Environmental sound awareness
  • Better modulation of voice
  • Possibilities of improvement

Where we’ve been Candidacy: Adult

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1985

Age: 18 yrs+ Hearing loss: bilateral profound post-lingual Speech recognition: 0% words or sentences with HAs Hearing aid use: 6 months

  • First outcomes reported pre-op vs. post-op
  • Comparisons of HA users and CI users
  • Results on CI outcomes in patients with more

hearing pre-op

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Where we’ve been Candidacy: Adult

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Candidacy: Adult

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Figure 2. Advances in technology and signal processing in cochlear implants have resulted in improved performance outcomes. Shown are group mean scores for CUNY and HINT sentences in quiet and CNC monosyllabic words from multiple sources: Skinner et al. (1994), Skinner et al. (1991);Pijl et al. (2009).

Huart, 2009

Where we are Candidacy: Adult

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Today

Age: 18 yrs+ Hearing loss: bilateral MODERATE – PROFOUND, post-, peri- or pre-lingual Speech recognition: ≤50% on sentences in ear to be implanted and ≤60% best aided/contralateral ear

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  • Speech scores can approximate normal hearers
  • Near ceiling performance at 3 - 6 months

experience

  • Updated speech battery (MSTB 2011)

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Where we are Candidacy: Adult

Gifford, 2008

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Candidacy: Pediatric

1990

Minimum age: 2 yrs Hearing loss: profound Communication: 0% words or sentences with HAs Hearing aid use: 6 months

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Candidacy: Pediatric

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Today

Minimum age: 12 – 23 mos Hearing loss: <24 mos prof HL; ≥24 mos sev-prof Communication: 30-40% word or sentence scores Hearing aid use: 3-6 months

Candidacy: Pediatric

  • Lower minimum age

– Higher communication performance – Higher scores on all language measures

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Word Learning

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Houston, et al. 2012

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Will Older Children Catch Up?

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Nicholas & Geers, 2007

Candidacy: Pediatric

  • More hearing

– Children with poorer hearing pre-CI had lower language skills at 3.5 yrs – Accounted for almost 60% of variance in language performance

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Nicholas and Geers, 2006

Candidacy: Pediatric

  • Reduced HA trial period
  • Children diagnosed and using hearing aids at the earliest ages

experienced longer periods of hearing aid use before implantation.

  • Children with greater aided residual hearing also experienced longer

hearing aid trials before implantation.

  • These data suggest long periods of hearing aid use prior to cochlear

implantation may not always be the most beneficial course of action for young children who may be CI candidates.

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Where we are Referral Warranted

  • Fluctuating hearing loss

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Enlarged Vestibular Aqueduct

  • Most common imaging finding
  • Excellent candidates for CI

– Early referral for patients with progressive/fluctuating loss

  • Variable outcomes when associated with other

cochlear malformations

  • Surgical risk of CSF gusher

– Managed intra-operatively – Has no significant effect on speech outcomes (Adunka, et al., 2012)

Audiogram (Pre-Eval)

Word Recognition RE: 4% LE: 84% PTA RE: 72 dB HL LE: 105 dB HL

Drop in RE hrg 1 mo ago following head injury Increased tinnitus since drop in hrg

Audiogram (CI Eval)

Aided Speech CNC AzBio-Q/+10 RE: 0% LE: 60% B: 50% 58% / 42%

Audiogram (CI )

Speech Perception 1 mo CNC AzBio-Q/+10 CI: 56% 75% / 32% Speech Perception 3 mos CNC AzBio-Q/+10/+5 CI: 74% 71%/57%/17% CI+ HA: 96% 100%/88%/73%

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Ménière’s Disease

  • Significant improvement

– Even with previous chemical or surgery treatment

  • Results similar to other post-lingually deaf

adults

  • Improvement in tinnitus
  • Most achieve stable hearing

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Lustig, et al., 2003

Where we are Referral Warranted

  • Fluctuating hearing loss

– EVAS – Meniere’s

  • Asymmetrical hearing loss

– Implant poorer ear – Bimodal listeners

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Where we are Referral Warranted

  • Fluctuating hearing loss

– EVAS – Meniere’s

  • Asymmetrical hearing loss

– Implant poorer ear – Bimodal listeners

  • Auditory Neuropathy Spectrum Disorder

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Auditory Neuropathy

  • No progress with auditory or language skills

– refer for CI evaluation – CI may offer neural synchronization

  • Outcomes are variable

– Comparable to SNHL in those without other medical/cognitive issues – ? Contraindicated in hypoplasia/aplasia of cochlear nerve – Counseling is key

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Where we are Referral Warranted

  • Fluctuating hearing loss

– EVAS – Meniere’s

  • Asymmetrical hearing loss

– Implant poorer ear – Bimodal listeners

  • Auditory Neuropathy Spectrum Disorder
  • WRS ≤ 50%

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Where we are Referral Warranted

  • Fluctuating hearing loss

– EVAS – Meniere’s

  • Asymmetrical hearing loss

– Implant poorer ear – Bimodal listeners

  • Auditory Neuropathy Spectrum Disorder
  • WRS ≤ 50%
  • Ski-slope hearing loss

– Hybrid/EAS – Improved hearing in noise, music quality

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Ski-slope Hearing Loss

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Cochlear Malformations: CI Candidacy

  • Candidate

– Common cavity – Cochlear hypoplasia – Incomplete partition – SCC dysplasia – Enlarged Vestibular Aqueduct

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  • Not candidate

– Complete labyrinthine aplasia – Cochlear aplasia – Absent auditory nerve

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Where we are going Emerging Indications

  • <12 months
  • SSD/Unilateral

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Where we are going Emerging Indications

  • <12 months

– What happens when there is no access to auditory information in the first year of life? – Cognitive mechanisms/language processes – Sensitive periods

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Emerging indications/Expanding Criteria

  • <12 months

– Improved phonological skills – Superior speech understanding – Language skills growth rate similar to normal-hearing peers – Support non-verbal cognitive development (Coletti, 2011)

  • Risks

– Minimalized by experienced pediatric surgeons and anesthesiologists

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Where we are going Emerging Indications

  • <12 months
  • SSD/Unilateral

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Where we are going Emerging Indications

  • <12 months
  • SSD/Unilateral

– Less difficulty hearing in noise – Some benefit for localization – Reduced tinnitus – ? Hearing quality – ? Binaural benefits

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Success

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Summary

  • Patients may have complex issues that need to

be fully evaluated in the CI work-up

  • Early referral of children for CI is best
  • Moderate to profound HL indicates referral
  • Less than fair WRS warrants referral
  • Refer any patient with PTA and WRS

discrepancy

Thank you!

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References

  • available upon request

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